Certain ear problems are common in people with Myhre syndrome. In this handout, you will learn about ear problems, including hearing loss, and how doctors diagnose and treat them in people with Myhre syndrome.

How Common are Ear Problems in People with Myhre Syndrome?

Ear problems are very common in children with Myhre syndrome.

What are Common Ear Problems in People with Myhre Syndrome?

Several ear problems are common in people with Myhre syndrome:

  • Extra ear wax. This may require removal by your pediatrician or an ear doctor.
  • Fluid in the ears. This can happen from an ear infection, or from a buildup of fluid behind the eardrum (a thin membrane that separates the outer ear from the middle ear).
  • Conductive hearing loss. This occurs when the path from the outer ear into the inner ear is blocked or damaged. This can occur with an infection, chronic fluid or wax.
  • Sensorineural hearing loss. This means that the nerve that allows normal hearing is not working as well.
  • Mixed hearing loss. This refers to a combination of both conductive and sensorineural problems.
  • Abnormal ear position or size. This is common in Myhre syndrome and typically mild.

Can Ear Surgery Be Performed on People with Myhre Syndrome?

In general, doctors try to avoid surgery in children with Myhre syndrome due to the risk of excessive scarring. Each child should be evaluated based on their problems. Doctors generally recommend inserting ear tubes in children who meet specific criteria.

A PE (pressure equalizing) tube is a tiny tube surgically placed within the eardrum through a small incision. It helps prevent fluid build-up behind the eardrum. This is the most common ear surgery in children.

For most children, this surgery can be done without endotracheal intubation (a breathing tube placed down the throat). Typically, children are able to go home on the same day if there is no intubation. Children who require intubation should be monitored overnight.

Sometimes, ear tubes need to be replaced. This is determined by the doctor who placed the tubes after they fall out or if they become blocked.

This picture shows different parts of the outer, middle, and inner ear.
The ear is made up of many different parts. Ear problems can affect any part of outer or inner ear.

 

Rev. 4/2020. Image courtesy of the CDC®. MassGeneral Hospital for Children and Massachusetts General Hospital do not endorse any of the brands listed on this handout. This handout is intended to provide health information so that you can be better informed. It is not a substitute for medical advice and should not be used to treatment of any medical conditions.